Malignant peripheral nerve sheath tumour metastatic to the orbit.

PURPOSE: To present a case of malignant peripheral nerve sheath tumour (MPNST) metastatic to the orbit.

METHOD/

RESULTS

The authors describe a 29-year-old woman with disseminated MPNST who presented with acute right orbital inflammation. Computerized tomography revealed a superolateral mass with a central radiolucent area. At biopsy, the mass was primarily subperiosteal and histology showed a spindle cell, S100-positive MPNST consistent with the primary tumour.

CONCLUSION

This is the second reported case of MPNST metastatic to the orbit and illustrates that an inflammatory presentation is possible in this aggressive malignancy.