Association of bilateral internuclear ophthalmoplegia and myelomeningocele with Arnold-Chiari malformation, type II.

We describe the unusual association of long-standing repaired myelomeningocele, hydrocephalus, and Arnold-Chiari malformation with bilateral internuclear ophthalmoplegia in a young man. A rarely reported association, this case emphasizes the need for further neuroradiologic evaluation to determine the possibility of third-ventricle enlargement with worsening hydrocephalus.