Compression of the Porta Hepatis in a Patient With Hepatic Cysts Secondary to Autosomal Dominant Polycystic Kidney Disease: A Case Report.

Autosomal dominant polycystic kidney disease (ADPKD) is a genetic disorder characterized by cyst formation in the kidneys and other organs: most commonly the liver, pancreas, and seminal vesicles. Hepatic cysts are one of the most common extrarenal manifestations of ADPKD, but generally remain asymptomatic. Rarely, they can cause mass effect leading to biliary obstruction, portal hypertension, or compression of adjacent vascular structures. We present the case of a 67-year-old woman with ADPKD, large hepatic cysts causing compression of the porta hepatis, and biliary strictures requiring stenting, in the absence of another accompanying liver disease.