Case report: When Behçet's disease meets multizonal outer retinopathy and retinal pigment epitheliopathy: longitudinal multimodal imaging of an overlap phenotype.

PURPOSE: To report a rare case of overlapping features of Behçet's uveitis and multizonal outer retinopathy and retinal pigment epitheliopathy (MORR), documented by longitudinal multimodal imaging.

METHODS

A single case report.

RESULTS

A 37-year-old male presented with unilateral, painless, progressive vision loss and a history of recurrent oral ulcers. Multimodal imaging with longitudinal follow-up documented bilateral, progressive outer retinopathy concurrent with retinal vasculitis. These features characterize an acute progressive episode not previously described.

CONCLUSION

This case highlights the importance of multimodal imaging and reminds clinicians to remain vigilant to possible concurrent outer retinopathy in Behçet's uveitis. Furthermore, given the favorable treatment response observed here, this case also offers a reference for the therapeutic strategy of MORR.