Right ureterovesical junction cyst associated with ipsilateral renal agenesis: a case report of a possible Wolffian duct maldevelopment.

INTRODUCTION

Right ureterovesical junction cyst associated with ipsilateral renal agenesis is an extremely rare congenital anomaly of the male genitourinary tract, likely resulting from abnormal development of the Wolffian duct and ureteric bud. We report the case of a 35-year-old man with a one-year history of progressive dysuria. Contrast-enhanced computed tomography (CT) revealed right renal agenesis and cystic dilatation of the intramural segment of the right ureter protruding into the bladder cavity, with the proximal ureter showing tortuosity and atresia. The contralateral kidney and ureter were normal. The patient underwent laparoscopic right ureterectomy combined with transurethral bladder exploration and left ureteral stent placement. Histopathological examination confirmed a ureterovesical junction cyst with chronic inflammation and cystic wall change. The postoperative course was uneventful.

CONCLUSION

This case highlights a rare Wolffian duct-related developmental anomaly distinct from classical Zinner syndrome, emphasizing the importance of recognizing atypical presentations for accurate diagnosis and optimal surgical management.