Angiomyolipoma Suspected to be the Lobular Capillary Hemangioma in the Nasal Cavity.

Angiomyolipoma (AML), composed of smooth muscle cells, blood vessels, and adipose tissues, belongs to a family of tumors originating from perivascular epithelioid cells. Angiomyolipoma most commonly arises in the kidney but is extremely rare in the nasal cavity. Angiomyolipoma is classified into hepatorenal and mucocutaneous AML. Mucocutaneous AML is defined as AML originating from the skin and nasopharyngeal mucosa. Mucocutaneous AML should be distinguished from hepatorenal AML because hepatorenal AML has a malignant potential. Moreover, mucocutaneous AML must be considered in the differential diagnosis for unilateral nasal mass despite being a rare disease. The authors present the case of a 70-year-old woman with mucocutaneous AML who complained of right epistaxis. Although she had a history of hypertension and acute myocardial infarction, it was not related to tuberous sclerosis. Endoscopic examination revealed a round and reddish mass protruding from the right inferior meatus. She underwent endoscopic resection without complications. She had no recurrence for 15 months.