Juvenile ankylosing spondylitis unmasked by severe aortic regurgitation and subaortic bump.

Enthesitis-related arthritis is a subtype of juvenile idiopathic arthritis that may precede or later progress to ankylosing spondylitis in adulthood. We describe a case of enthesitis-related arthritis diagnosed based on characteristic echocardiographic findings of aortitis, subaortic bump and severe aortic regurgitation.