[Idiopathic retroperitoneal fibrosis:clinical characteristics of 61 cases and literature review.].

OBJECTIVE

We reviewed the data of 61 cases with idiopathic retroperitoneal fibrosis (IRF). The purpose was to understand the feature of the disease in order to improve its diagnosis and treatment.

METHODS

The clinical data of 61 cases discharged from our hospital were analyzed retrospectively.

RESULTS

IRF was seen in male higher than in female (3.7:1), the mean age was 55.7 years. One case was complicated with polymyositis, two cases had family history. Back pain and abdominal pain were most commonly onset symptoms. 34 patients were treated with surgery, 10 patients treated with corticosteroid or combined with immunosuppressive agents or tamoxifen, 4 patients treated with surgery combined with corticosteroid. Two patients were died, other patients responded well to managements.

CONCLUSION

Each of the three different therapeutic approaches were effective. Long-term low dose steroids therapy could prevent recurrence.