[Pericarditis, arthritis, camptodactyly syndrome: four decades after its original description].

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome (CACP) syndrome is a clearly underdiagnosed cause of constrictive pericarditis and degenerative hip arthropathy. We reviewed all cases of CACP syndrome described in the PubMed database. Founded on this review, two simple clinical maneuvers are proposed to diagnose CACP syndrome with high degree of certainty. This review also proposes that the clear pathogenetic mechanisms discovered on rare monogenic condition as CACP may aid in understanding common heterogeneous diseases such as osteoarthritis.