Lipodystrophia Centrifugalis Abdominalis Infantilis: A Case in a Vietnamese Patient.

BACKGROUND

Lipodystrophia centrifugalis abdominalis infantilis (LCAI) is an uncommon dermatological condition characterized by a centrifugally expanding area of lipoatrophy involving the lower abdominal area and is frequently associated with inguinal lymphadenopathy. The average age of onset is 4 years and female individuals from Japan, China, and Korea are affected more often.

OBJECTIVES

To report the first case of LCAI in a Vietnamese patient.

METHODS

A complete clinical assessment was done and a biopsy from the affected area was performed.

RESULTS

There was an atrophic, slightly hyperpigmented patch at the lower abdomen with prominent underlying vasculature. Inguinal lymphadenopathy was noted on the ipsilateral side. A biopsy showed a lobular panniculitis with fat necrosis and lymphohistiocytic infiltrate with scattered plasma cells and multinucleated giant cells.

CONCLUSION

To our knowledge, this is the first reported case of LCAI in a Vietnamese patient.