Noonan's syndrome associated with cake kidney.

Noonan's syndrome is an established clinical entity. These cases are often associated with correctable cardiac abnormalities, cryptorchism, and abnormal urinary tract. Herein is described the first case of Noonan's syndrome associated with cake kidney. The very high incidence of renal tract abnormalities in association with this syndrome warrants an excretory urogram in these cases for proper evaluation and management.