Nevoid basal cell carcinoma syndrome: review of the literature and report of a case.

Any patient who has multiple cystic lesions of the jaws should be evaluated for the presence of other signs of nevoid basal cell carcinoma syndrome. The workup should include consultations with specialists in neurology, radiology, dermatology, medical genetics, and any other specialty areas where signs of symptoms may appear. It is not unusual for the oral surgeon to be the first practitioner to see such a patient, because initial complaints often refer to pain and swelling for an infected jaw cyst. The workup of this case and its treatment are typical for a patient with nevoid basal cell carcinoma syndrome.