The "turban" nevoid basal cell syndrome. Current management with surgery, chemotherapy and immunotherapy.

"Turban" nevoid basal cell syndrome is a congenital disease that presents with multiple subepidermal epitheliomas, primarily on the scalp. Other secondary findings may be present such as cysts in the mandible and bifid synostotic rib. A combination of treatments proved beneficial in this disease. Surgical excision was used for treatment of large symptomatic lesions such as painful ulcerating and enlarging tumors. Chemotherapy was used to arrest and cause regression of small and dormant lesions. Immunotherapy was used to control the primary disease. Such treatment cured most of the disease and offered a fruitful life to the patient, who is presented to illustrate this multiple disciplinary approach.