[Lipoidproteinosis].

We report the first case of L.P. in our country with typical lesions of skin, pharyngeal and laryngeal mucous membranes. Our observation did not indicate any history of consanguinity nor family incidence, nor visceral engagement. The hepatic biopsy was normal. Connected with the main illness we found a radiopaque area in the right frontal bone which engaged the interior and exterior walls, and a calcification nodule in the base of the right maxillary sinus.