Frosted branch angiitis, presumably related to dermatomyositis.

PURPOSE: To report the first case of frosted branch angiitis associated with dermatomyositis in a Korean woman.

METHODS

Case report.

RESULTS

A 42-year-old woman with history of dermatomyositis presented with unilateral decreased visual acuity. Fundus examination showed findings consistent with frosted branch angiitis. After 1 month of oral prednisolone, the patient made significant visual recovery with near complete resolution of vascular sheathing.

CONCLUSIONS

To the best of the authors' knowledge, this is the first case of frosted branch angiitis associated with dermatomyositis. Dermatomyositis should be considered in the differential diagnosis of patients presenting with frosted branch angiitis.