Laparoscopic management of splenogonadal fusion with contralateral crossed ectopic preperitoneal testis presenting as ambiguous genitalia.

We report an extremely rare case of ambiguous genitalia presenting with bilateral non-palpable cryptorchidism and scrotal hypospadias with long-term follow-up. The patient had discontinuous splenogonadal fusion of the left testis and an ectopic preperitoneal right testis located to the left of the urinary bladder. Laparoscopic bilateral orchidopexy was performed after the excision of splenic tissue on the left side. Chordee correction and urethroplasty were performed subsequently. To the best of our knowledge, a similar case of male disorder of sexual differentiation with preservation of the testicular tissue has not been reported before.