[Epidural anesthesia for Cesarean section in a patient with von Hippel-Lindau syndrome].

Von Hippel-Lindau (VHL) disease is an autosomal dominant disorder with variable penetrance. It is mainly characterized by haemangioblastomas of the retina and central nervous system. Because of physiological effects of uterine contractions, labour and spontaneous vaginal delivery increase the risk of disrupting central nervous system haemangiblastomas. We report the case of a 28-year-old woman with an history of VHL disease who had an epidural anaesthesia for labour and for Caesarean section performed because of failure to progress and of fetal distress. The overall maternal and neonatal outcomes were excellent.