The success of the Cystic Fibrosis Registry of Turkey for improvement of patient care.
Обработка статьи · этапы, ошибки и управление
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Asfuroglu Pelin, Sismanlar Eyuboglu Tugba, Aslan Ayse Tana, Gursoy Tugba Ramasli, Emiralioglu Nagehan, Yalcin Ebru, Kiper Nural, Sen Velat, Sen Hadice Selimoglu, Altintas Derya Ufuk, Ozcan Dilek, Kilinc Ayse Ayzit, Cokugras Haluk, Baskan Azer Kilic, Yazan Hakan, Erenberk Ufuk, Dogan Guzide, Unal Gokcen, Yilmaz Asli Imran, Keskin Ozlem, Arik Elif, Kucukosmanoglu Ercan, Irmak Ilim, Damadoglu Ebru, Ozturk Gokcen Kartal, Gulen Figen, Basaran Abdurrahman Erdem, Bingol Aysen, Cekic Sukru, Sapan Nihat, Kilic Gonca, Harmanci Koray, Kose Mehmet, Ozdemir Ali, Tugcu Gokcen Dilsa, Polat Sanem Eryilmaz, Hangul Melih, Ozcan Gizem, Aydin Zeynep Gokce Gayretli, Yuksel Hasan, Topal Erdem, Ozdogan Sebnem, Caltepe Gonul, Suleyman Ayse, Can Demet, Ekren Pervin Korkmaz, Bal Cem Murat, Kilic Mehmet, Cinel Guzin, Cobanoglu Nazan, Pekcan Sevgi, Cakir Erkan, Ozcelik Ugur, Dogru Deniz
Аннотация
METHODS: Age at diagnosis, current age, sex, z-scores of weight, height and body mass index (BMI), neonatal screening results, pulmonary function tests, history of meconium ileus, medications, presence of microorganisms, and follow-up were evaluated and compared to data of people with CF represented in both 2017 and 2019 registry data.
RESULTS: There were 1170 people with CF in 2017 and 1637 in 2019 CF registry. Eight hundred and fourteen people were registered in both 2017 and 2019 of whom z-scores of heights and BMI were significantly higher in 2019 (p = 0.002, p =0.039, respectively). Inhaled hypertonic saline, bronchodilator, and azithromycin usages were significantly higher in 2019 (p =0.001, p = 0.001, p = 0.003, respectively). The percent predicted of forced expiratory volume in 1 sec and forced vital capacity were similar in 2017 and 2019 (88% and 89.5%, p = 0.248 and 84.5% and 87%, p =0.332, respectively). Liver diseases and osteoporosis were significantly higher, and pseudo-Bartter syndrome (PBS) was significantly lower in 2019 (p = 0.011, p = 0.001, p = 0.001, respectively).
CONCLUSIONS: The z-scores of height and BMI were higher, the use of medications that protect and improve lung functions was higher and incidence of PBS was lower in 2019. It was predicted that registry system increased the care of people with CF regarding their follow-up. The widespread use of national CF registry system across the country may be beneficial for the follow-up of people with CF.