Giant hydronephrotic kidney in adolescence- A rare case report and a review of the literature.

Giant hydronephrotic kidney is a rare form of obstructive uropathy in adolescents. We report a 19 year old girl with huge abdominal distention secondary to hydronephrotic kidney. The cystic swelling occupied whole of the abdominal cavity with other structures being compressed. She presented with progressive distention of abdomen with early satiety. Subsequently ultrasonological and CT scan evaluation revealed a giant hydronephrosis of right kidney occupying almost whole abdomen. Such presentation of PUJ obstruction is rare. We present this case in which percutaneous nephrostomy with slow decompression was done as initial treatment to relieve symptoms and prevent complications.