Successful treat-and-repair strategy in a 5 year old with partial anomalous pulmonary venous connection, atrial septal defect, and severe pulmonary hypertension.

We report the case of a 5-year-old boy with severe pulmonary arterial hypertension due to partial anomalous pulmonary venous connection and atrial septal defect. Sequential combination therapy using multiple pulmonary vasodilators enabled safe surgical repair. In this case of severe pulmonary arterial hypertension-associated with partial anomalous pulmonary venous connection and atrial septal defect-the treat-and-repair strategy proved effective.