One-stage repair of Taussig-Bing anomaly in a neonate with aortic arch hypoplasia and single coronary artery.

In 1949, Helen Taussig and Richard Bing described the Taussig-Bing anomaly, which is a form of conotruncal malformation in which there is a double outlet right ventricle and subpulmonic ventricular septal defect with side-by-side great arteries. Controversy exists regarding whether or not the presence of double coni should be included as part of the diagnosis, and it is not unusual to have associated aortic arch hypoplasia with or without coarctation and coronary arterial anomalies that may complicate the repair and increase surgical risks. Debate has been ongoing between single- versus two-stage repair of Taussig-Bing anomaly, especially in small neonates. The arterial switch operation appears to be the preferred approach, especially when the great arteries are side by side. In this video tutorial we present the technical details of a single-stage neonatal repair of Taussig-Bing anomaly combined with aortic arch hypoplasia and the presence of a single coronary artery.