Right Pulmonary Artery Agenesis in an Adult: A Case Report of Silent Pulmonary Hypoplasia.

Pulmonary artery agenesis is a rare congenital malformation and most often affects the right pulmonary artery. It is associated with other congenital anomalies such as tetralogy of Fallot, or it can be isolated and revealed in a less dramatic presentation in adulthood. We report in this work a case in an adult. This is a 40-year-old patient admitted for chest tightness and pain. The clinical examination was normal. Chest CT angiography and echocardiography confirmed the diagnosis of right pulmonary artery agenesis without other associated malformations. The patient has been followed for one year with good progress. Early diagnosis allows for planned and appropriate management.