Use of right atrial wall to repair severely dysplastic tricuspid valve in an infant with Ebstein's anomaly.

The management of infants with Ebstein's anomaly is challenging and requires complex involvement of the multidisciplinary team. Surgical repair technique is dependent on the degree of tricuspid leaflet dysfunction and the decision to undergo univentricular or biventricular repair. Patients with a severely dysplastic tricuspid valve are less suited to a cone repair alone and require leaflet reconstruction. Currently used patch materials include autologous untreated pericardium and treated pericardium, with limitations such as unpredictable shrinkage and no growth potential, respectively. To overcome these challenges, we used living autologous wall of the right atrium to reconstruct the tricuspid valve leaflets in a 1-year-old girl with Ebstein's anomaly and a severely dysplastic tricuspid valve.