Anesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study.

Pentalogy of Cantrell compiles the union of five anomalies including defects of the midline abdominal wall, lower sternum, anterior diaphragm, diaphragmatic pericardium, and any form of intra-cardiac pathology 1. The intra-cardiac defects associated commonly are ventricular septal defects, followed by atrial septal defects, Tetralogy of Fallot, and pulmonary stenosis 2. It is also a rare syndrome with an estimated incidence of 1:65,000 to 200,000 live births.3 4 Here in we present a case of a 4-year-old male patient, diagnosed with Pentalogy of Cantrel was referred to our institute with chief complaints of breathlessness associated with cyanosis on exertion. He has ectopia cordis along with omphalocele since birth.