Neonatal repair of atypical double outlet right ventricle.

BACKGROUND

A complex and rare form of double outlet right ventricle needs careful attention when choosing the optimal strategy for repair.

AIM OF THE STUDY: To point out retrospectively what could have been done differently in our unique patient.

METHODS

Primary repair was arranged in a neonate with double outlet right ventricle (of a non-committed ventricular septal defect type and lack of the outlet septum between the semilunar valves) with right aortic arch and dextro-malposition of great arteries.

RESULTS

We managed to achieve intraventricular rerouting via a right ventricular incision concomitantly with the arterial switch maneuver. The patient is doing well with an excellent hemodynamic status.

CONCLUSIONS

We considered that the radical approach we chose appeared to be sensible in this particular patient, although some other options could have been available.