[Doege-Potter syndrome is a solitary fibrotic tumour often leading to hypoglycaemia].

Doege-Potter syndrome is a rare paraneoplastic syndrome, in which a solitary fibrotic tumour secretes insulin-like growth factor II leading to hypoglycaemia. In this case report, a 70-year-old woman known with a big intra-abdominal tumour was admitted to hospital, unconscious with a blood sugar of 1.8 mmol/l. She was treated with intravenous glucose until surgery, which cured her temporarily. After four months she had relapse and no effect of chemotherapy. Surgery is the only curative treatment for Doege-Potter syndrome, which is important to remember, if a patient has unexplained hypoglycaemia and a tumour.