Congenital absence of left pulmonary artery in association with isolated pulmonary valvular stenosis:

Congenital absence of either of the pulmonary arteries is a rare condition but an entity known for almost one and half century. Unilateral absence of a pulmonary artery commonly occurs in association with other congenital cardiac lesions, but can also occur alone. Differential vascularity on plain chest radiograph is the usual clue to the diagnosis. Here, a 14 month old patient with congenital absence of the left pulmonary artery in association with isolated pulmonary valve stenosis is described.