Double-chambered right ventricle associated with infective endocarditis complication of the pulmonary valve: surgical management.

Double-chambered right ventricle (DCRV) is a rare congenital heart disease characterized by the presence of anomalous muscle bundles, which divide the right ventricle into two chambers: a high-pressure proximal chamber and a low-pressure distal chamber. Most DCRV patients are diagnosed and treated during childhood, and presentation in adulthood is not common. Many congenital heart diseases are often associated with other complications such as infective endocarditis (IE). Right-side endocarditis, which usually involves infection of the tricuspid valve, is uncommon, and endocarditis of the pulmonary valve is extremely rare. We report a 51-year-old woman with undiagnosed DCRV and ventricular septal defect associated with pulmonary valve endocarditis. The diagnostic evaluation and the surgical management are discussed.