"True agonadism" and its relation to other forms of sex reversal in males.

In a phenotypic (XY karyotype) eunuchoid female aged 24, external genitalia were represented by completely fused underdeveloped scrotolabial folds and a 1-cm-long phallus with phallic urethra. At laparotomy, only rudimentary fallopian tubes and rudimentary wolffian ducts and wolffian body, but no testes, epididymis, uterus or vagina, were found. The patient fulfills the criteria for "true agonadism." This syndrome is considered a distinct form of a wider category of male pseudohermaphroditism, which results from sudden complete testicular arrest taking place not earlier than the second half of the third month of embryonic development.