Severe Aortic Insufficiency in a Patient with a Functionally Bicuspid Quadricuspid Aortic Valve.

• Quadricuspid aortic valve is an uncommon congenital cardiac malformation often discovered incidentally at the time of valve surgery or at autopsy. • It is commonly associated with progressive aortic regurgitation, with nearly half of affected patients requiring aortic valve replacement surgery during their lifetime. • Dilatation of the aortic root and ascending aorta has also been reported in a significant number of affected patients.