Pulmonary Endarterectomy for Chronic Thromboembolic Pulmonary Hypertension Secondary to Expanded Polytetrafluoroethylene Valved Pulmonary Conduit Thrombosis.

BACKGROUND

There is no consensus on the preferred conduit for right ventricular outflow tract (RVOT) reconstruction for congenital cardiac disease.

CASE SUMMARY: We present a case of a 21-year-old woman with history of tetralogy of Fallot presenting with recurrent graft thrombosis and pulmonary emboli in the setting of RVOT reconstruction with a 20-mm expanded polytetrafluoroethylene (ePTFE) valved conduit (GORE PV1, W.L. Gore & Associates). A diagnosis of chronic thromboembolic pulmonary hypertension was made, and the patient underwent pulmonary endarterectomy and conduit exchange with a pulmonary homograft.

DISCUSSION: The novelty and clinical significance of this report lies in the confirmation of thrombosis of a large-diameter ePTFE valved pulmonary conduit (20 mm) and its implications for monitoring and need for further optimization of thromboprophylaxis strategies in this population.