[Total anomalous pulmonary venous connection with an unusual drainage vein from the right lung to the innominate vein;report of a case].

We encountered a case of total anomalous pulmonary venous connection with a drainage vein following an unusual course. The drainage vein, after emerging from the right lung, crossed the midline and drained into the innominate vein. Along the course of this vein, severe stenosis was present in the region wedged between the aortic arch and pulmonary artery, leading to severe pulmonary congestion. The common pulmonary vein was well developed. There was no other intracardiac malformation except atrial septal defect. No heterotaxy syndrome associated. Because echocardiography was unable to provide a complete picture of the pulmonary veins and drainage veins, multidetector-row computed tomography was performed to ascertain the anatomy. Emergency surgical intervention was carried out and anastomosis of the common pulmonary vein to the left atrium was performed. The postoperative course was favorable.