Laparoscopic bilateral gonadectomy in a phenotypic woman with a form of Leydig cell hypoplasia.

A 22-year-old phenotypic woman with an XY karyotype underwent laparoscopic gonadectomy after a comprehensive evaluation for primary amenorrhea. Pathology revealed primitive testicular support elements with absent Leydig cells bilaterally. This case illustrates the fact that, with a thorough preoperative workup, patients expressing various forms of male pseudohermaphroditism can now be treated appropriately by laparoscopy instead of laparotomy.