[Darier-Ferrand Dermatofibrosarcoma In Point "G" University Hospital].

INTRODUCTION

Darier-FERRAND dermatofibrosarcoma is a slow-growing fibrous skin tumor with a very high risk of local recurrence but low metastatic potential.

OBJECTIVE

To determine the epidemiological, clinical, and therapeutic characteristics and analyze the treatment outcomes.

METHODOLOGY: This was a retrospective, cross-sectional study from January 2018 to December 2023, including patients operated on for histologically confirmed Darier-FERRAND dermatofibrosarcoma (DFS).

RESULTS

Eight patients with DFS were included. The mean age was 49 years. The sex ratio was 7M/1F. Four were experiencing their first episode, three had undergone surgery once for the same tumor, and one patient was experiencing a second recurrence. The masses were located on the thigh in five cases, two on the trunk, and one on the left arm. The mean tumor size was 12.8 cm. The mean tumor duration was 18.1 months. The treatment decision was based on the presumptive diagnosis. Management was surgical in all patients. The surgical procedure performed in all patients was tumor excision in a healthy area with a 4 cm resection margin.

CONCLUSION

Dermatofibrosarcoma of Darier-Ferrand type is a rare skin tumor. Its progression is very slow, with a very high risk of local recurrence if surgical excision is incomplete, hence the importance of wide surgical excision.