Double uteri with cervicovaginal agenesis.

OBJECTIVE

To report results of managing complex malformation of the genital tract and to validate a newer classification (vaginal, cervix, uterus, adnexa-associated malformation [VCUAM]) for describing such complex anomalies.

DESIGN

Case report.

SETTING

University hospital.

PATIENT(S): A patient with complex genital malformation.

INTERVENTION(S): Laparotomy, double hysterectomy, and vaginal reconstruction with use of bilateral neurovascular pudendal thigh flaps. Use of VCUAM classification for description of the anatomy of malformation.

MAIN OUTCOME MEASURE(S): Creation of a neovagina and accurate and complete description of the anomaly.

RESULT(S): Relief of pelvic pain and creation of patent and sensate vagina retaining the innervations of the erogenous zones. The VCUAM classification could accurately depict complex anatomic variations.

CONCLUSION(S): Vaginal reconstruction with use of bilateral neurovascular pudendal thigh flaps yields good postoperative results. The VCUAM classification reflects anatomic variations in external and internal organs precisely.