Cutaneous lung tissue heterotopia.

AIMS: We describe the clinical and pathological findings of a previously unreported cutaneous lung tissue heterotopia in a child.

CASE DETAILS: The 3-year-old female patient developed a 8-mm secreting papule over her left scapula. Pathological examination revealed a lesion composed of bronchioles and alveoli within the subcutis and the dermis, with bronchiolar connection to the epidermis. Alveolar type II cells indicating full pulmonary differentiation were detected with a monoclonal antibody (AMH 152).

CONCLUSIONS

The described features suggest that this lesion is a unique variant of rarely observed bronchus-like entities of the skin, designated as cutaneous bronchogenic cysts or cutaneous branchial cleft cysts.