Ectopic respiratory epithelium associated with multiple malformations.

We report a patient with unique cutaneous plaques of ectopic respiratory epithelium. The epithelium was located superficially as raised erythematous plaques on the right lateral surface of the neck with some viscous secretion. Underlying branchial cysts or sinuses were excluded. The occurrence of ectopic respiratory epithelium was associated with congenital deafness and a hare-lip in our patient, suggesting multiple malformation during early embryonic development.