Late-Onset Cyanosis and Finger Clubbing in a 37-Year-Old Female with Ebstein's Anomaly and Atrial Septal Defect.

UNLABELLED: It is common to suspect Eisenmenger syndrome when patients with atrial septal defect (ASD) show cyanosis and clubbing. However, ASD accompanying Ebstein's anomaly frequently shows cyanosis without severe pulmonary hypertension, especially in the early period after birth. So the medical decision to decline surgical treatment in those patients should not be determined merely by clinical features such as cyanosis and clubbing. We report a case of a 37-year-old female with Ebstein's anomaly and secundum ASD who showed lip cyanosis and finger clubbing, but maintained normal pulmonary artery pressure and thus underwent successful surgical correction.

KEY WORDS: Atrial septal defect; Cyanosis; Ebstein's anomaly; Eisenmenger syndrome.