Persistent left SVC with absent right SVC: a rare anomaly.

A persistent left superior vena cava is an anomaly found in association with many congenital heart disorders. However its presence along with absence of the right superior vena cava is a very rare congenital anomaly. This anomaly has implications in various interventional procedures and in cardiac surgery. We present here a case with absence of the right SVC and a persistent left SVC found in association with an ostium secundum atrial septal defect.