Primary surgical correction of transposition of the great arteries and atrioventricular septal defect associated with left isomerism.

We report successful primary surgical repair of transposition of the great arteries (TGA) and complete atrioventricular septal defect (AVSD) associated with left isomerism {I,L,L} without pulmonary obstruction in a 1-month-old infant. The operative procedure consisted of an arterial switch and a two-patch repair of the AVSD. To the best of our knowledge, this is the first report of successful primary surgical repair of TGA and AVSD with left isomerism. Primary anatomic correction of this defect combination is feasible in patients with left isomerism.