Congenitally bicuspid aortic valve in brothers: coarctation of the aorta with a normally functioning aortic valve in one and no coarctation but severe aortic stenosis in the other.

Described herein are two brothers, both with a congenitally bicuspid aortic valve-one of which was stenotic and one of which functioned normally-and one with associated aortic isthmic coarctation. Summarized also are previously reported families with more than one member with a congenitally bicuspid aortic valve.