Ebstein's anomaly of the tricuspid valve complexities and strategies.

Ebstein's anomaly of the tricuspid valve is a fascinating but very complex congenital malformation with a wide spectrum of anatomic and clinical variations. A brief review is given of the clinical presentation and therapeutic options. We need further functional studies to understand the relationship between clinical severity and anatomic derangement. This will lead to better decision-making regarding the indications for and timing of surgery, which are still problematic.