[McKusick-Kaufman syndrome as a cause of acute abdomen in the neonatal period].

The McKusick-Kaufman-syndrome, also known by the name of hydrometrocolpos-hexadactyly syndrome, is an autosomal-recessive hereditary disease or spontaneous malformation. A hydrometrocolpos is formed in the process by a transversal vaginal septum and subsequently acts like an abdominal tumour to compress the iliac veins and to result in supravesical obstruction, eventually causing a condition of ileus and respiratory problems. Transvaginal drainage is used as primary therapy.