SURGICAL MANAGEMENT OF RETINAL DETACHMENT IN OSTEOGENESIS IMPERFECTA: CASE REPORT AND REVIEW OF THE LITERATURE.

PURPOSE: To describe a case of scleral buckling in a patient with severe (Type III) osteogenesis imperfecta.

METHODS

Single interventional case report of a 37-year-old woman, with clinically diagnosed osteogenesis imperfecta Type III, presenting with an inferior retinal detachment of the right eye. The patient was promptly treated with scleral buckling.

RESULTS

Long-term follow-up has shown a good clinical outcome, with no recurrence of the retinal detachment. Eighteen months postsurgery, an ischemic branch retinal vein obstruction has developed in the right eye, complicated by macular edema. The patient was treated successfully with bevacizumab injections, with restoration of visual acuity to 20/25.

CONCLUSION

Scleral buckle may provide a good surgical option in selected patients with osteogenesis imperfecta, yielding excellent anatomical and functional results.