Two cases of orbital lymphangioma associated with vascular abnormalities of the retina and iris.

PURPOSE: To report 2 patients with combined intraocular and orbital vascular abnormalities.

DESIGN

Two interventional case reports.

MAIN OUTCOME MEASURES: Clinical and pathologic findings. INTERVENTION/TESTING: Orbitotomy, fluorescein angiography, magnetic resonance imaging, and radiation therapy.

RESULTS

Two patients presented with vision loss, intermittent proptosis, and cosmetic deformity. These patients had orbital lymphangioma, ipsilateral retinal and iris vascular malformations, and smaller corneal diameter on the affected side.

CONCLUSIONS

The coexistence of these diverse vascular anomalies supports the established hypothesis of pluripotential orbital vascular anlagen. Disruptive influences of various types during embryogenesis or development may produce a variety of congenital orbital and intraocular vascular malformations.