Right ventricular endomyocardial fibrosis simulating Ebstein's anomaly.

A case of right ventricular endomyocardial fibrosis simulating Ebstein's anomaly is described. The clinical features, chest x-ray, electrocardiogram, echocardiogram, intracardiac electrogram, and the angiogram were all compatible with Ebstein's malformation. A correct diagnosis was subsequently made in the operating room. Reasons for the difficulties in the differential diagnoses of these two entities are discussed.