Ebstein's anomaly of the left atrioventricular valve with congenital corrected transposition of the great arteries. Diagnosis by intracavitary electrocardiography.

We present the findings in a 13-month-old infant with angiographically confirmed congenital corrected transposition of the great arteries and insufficiency of the left atrioventricular valve. Simultaneous intracavitary electrocardiographic and pressure recordings across the left atrioventricular valve were similar to those obtained in Ebsteins' anomaly and suggested Ebstein's disease of the left atrioventricular valve. To our knowledge, this is the first reported case with intracavitary electrocardiograms in a patient with congenital corrected transposition of the great arteries with Ebstein's malformation of the left atrioventricular valve. The usefulness of the simultaneous recording of the intracavitary ECG and pressure in the diagnosis by catheterization of Ebstein's anomaly of the left atrioventricular valve in patients with congenital corrected transposition of the great arteries is emphasized.