Outcome of Multi-Cystic Dysplastic Kidneys in Children.

BACKGROUND

Renal cystic diseases are important causes of chronic kidney disease (CKD).

OBJECTIVES

We report the pattern of renal cystic disease in children and evaluate the outcome of children with multicystic dysplastic kidney (MCDK).

PATIENTS AND

METHODS

Retrospective study of all children with cystic kidney diseases at King Abdulaziz University hospital from 2006 to 2014.

RESULTS

Total of 55 children (30 males); 25 MCDK, 22 polycystic kidney diseases (PKD), 4 nephronophthises and 4 renal cysts. Consanguinity was positive in 96.2%. MCDK and simple renal cyst patients had good renal function while PKD and nephronophthisis developed renal impairment. Most MCKD were diagnosed ante-natally, 16 of them were followed up for 3.4 (1.97) year. Their last creatinine was 33.9 (13.5) umol/L. MCDK was spontaneously involuted at mean age of 2.6 (1.3) years in 56%.

CONCLUSIONS

MCDK is the commonest cystic renal disease and diagnosed ante-natally in the majority of cases. It has a good prognosis.