[Uhl's anomaly: case description with hemodynamic study and autoptic report (author's transl)].

A 3 month's old baby with Uhl's disease is reported. The diagnosis was made by cardiac catheterization and angiographic evaluation of right atrial and ventricular chambers and was confirmed by autopsy and histopathological examination. The particular features which allow angiographic differentiation from Ebstein's anomaly are considered. On the grounds of anatomical, clinical, and prognostic aspects, it is proposed that the definition of Uhl's anomaly be reserved for cases in infancy only, using the term Osler's disease for adult cases.