Multidisciplinary approach to a Marfan syndrome patient with emphasis on cardiovascular complications.

BACKGROUND

Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFS patients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential.

CONCLUSION

Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.